This 36YO male was referred for asymptomatic unilateral fundus findings. He had a history of retinal reattachment surgery 13 years earlier. Vision was 20/40.
Optos color RGB imaging shows chorioretinal scarring with diffuse intraretinal pigment migration within the area of prior detachment, giving the appearance of pseudo-sector retinitis pigmentosa (RP). A demarcation line courses through the inferior macula. This just spares the central macula, thankfully leaving him with good central acuity.
Learning Points:
Photoreceptor loss from numerous causes, including blunt trauma, retinal detachment, macular telangiectasia, and RP, can allow for intraretinal RPE migration with this shared phenotype.
Unilateral RP is exceedingly rare and requires normal electrophysiologic findings and long-term observation to ensure delayed findings in the fellow eye.
