Wall of Fame

Is your case great enough to be selected for our Wall of Fame? If so, we’ll post your name and case here for the world to see!

10/23: Evgenii Chernov
Best Disease

9/24: Anjana Mirajkar and Manish Nagpal
Intraocular Foreign Body

8/24: Anjana Mirajkar and Manish Nagpal
Pseudopapilledema from leukemic optic nerve infiltration

7/24: Justin Grassmeyer, Ambar Faridi, and Brittany Heckerman
Lattice degeneration

6/24: Ogugua Okonkwo, Adekunle Olubola Hassan, Ayodele Harriman, Ogochukwu Sibeudu, and Idris Akintayo Oyekunle
Tuberculous serpiginous-like choroiditis

5/24: Seif Anwar
Inherited Retinal Disease

Sengül Özdek and Ece Özdemir Zeydanlı
Case of the Year winner!
Retinal Arteriovenous Malformation

4/24: Kanwaljeet Harjot Madan
Shaken baby syndrome

3/24: Ayushi Gupta and Vishal Agrawal
Benign familial fleck retina

2/24: Will Gibson
Retinal venous malformation

12/23: Anjana Mirajkar and Manish Nagpal
Central retinal artery occlusion with cilioretinal sparing

11/23: Anjana Mirajkar and Manish Nagpal
Harada’s Disease

10/23: Will Gibson
Posterior scleritis with chorioretinal folds

9/23: Shivraj Tagare and Nishant Maindargi
Valsalva retinopathy drained with YAG laser

8/23: Mohammad Abbas
Laser-induced retinal break and vitreous hemorrhage

7/23: Joe Yuenpang Cheung
Group-type congenital pigmented nevi of the RPE (bear tracks)

6/23: Gil Calvão-Santos and Keissy Sousa
Waardenburg Syndrome

5/23: Natasa Draca and Ratko Lazic
Tattoo-induced Uveitis

4/23: Veronika Matello and Barbara Parolini
Case of the Year winner!
The EmPuzzled Eye

3/23: Emma Oreskovic and Natasha Draca
Optic Nerve Pit

2/23: Anjana Mirajkar
Giant RPE Tear

11/22: Veronika Matello and Barbara Parolini
Choroidal Hemangioma Widefield OCT

8/22: Nivesh Gupta
Ischemic Central Retinal Vein Occlusion

7/22: Omar Mulki:
Choroidal Osteoma

3/22: Erdem Dinç
Is Temporary ILM Flap Sufficient for MH Closure?

1/22: Veronika Matello and Barbara Parolini
Case of the Year winner!
Choroidal Transplant for Subfoveal AMD MNV

12/21: Otis Hertsenberg
Optic Nerve Coloboma with Pit

11/21: David Kilpatrick
Frosted Branch Angiitis from Sarcoidosis

10/21: Kumar Chugani
Coats Disease

Best disease

Congratulations to Evgenii Chernov for submitting the Retina Rocks Case of the Month.Color photography of our patient’s right eye shows a partially scrambled Best lesion (images 1 and 2 top). OCT scanning through the superior lesion shows a mostly hyporeflective elevation of the neurosensory retina, with shaggy hyperreflective material along the posterior edge of the outer segments (red line/box). OCT scanning through the inferior lesion shows hyperreflective layering of the vitelliform material (yellow line/box). Similar findings were noted in their left eye (not shown). Best disease is associated with a mutation in the BEST1 gene, which encodes for the bestrophin-1 protein. Bestrophin-1, a calcium-activated chloride channel, is primarily found in the basolateral plasma membrane of the RPE. BEST1 mutations cause a variety of phenotypes, also including autosomal recessive bestrophinopathy, best vitelliform macular dystrophy, and autosomal dominant vitreoretinochoroidopathy. Our patient has progressed to the ‘scrambled egg’ appearance. The remaining vitelliform material gravitates inferiorly, often leaving an optically empty, hyporeflective space between the RPE and outer retina. Eventually the retina flattens over time with secondary outer retinal atrophy.

Case of The Month

Best disease