This 13YO female has unilateral disseminated patches of choroidal melanocytosis, but without anterior segment or skin abnormalities.
Learning Points:
Choroidal melanocytosis is part of the oculodermal spectrum, which occasionally includes pigmentation of the globe or periocular skin (Nevus of Ota, melanosis oculi).
There are increased dendritic melanocytes in the affected tissues following the distribution of the first and second branches of the trigeminal nerve.
Patients need ongoing monitoring since about 1 in 400 will develop uveal melanoma. Those who develop melanoma are twice as likely to undergo metastasis when compared to patients with uveal melanoma and no pre-existing melanocytosis.
