This asymptomatic patient was found to have a unique bilateral peripapillary chorioretinal atrophy called helicoid peripapillary chorioretinal degeneration.
Vision is usually normal, although central vision can rarely be affected if atrophy progresses through the fovea.
Learning Points:
Helicoid peripapillary chorioretinal degeneration is a benign autosomal dominant condition with degenerative wing or propeller-shaped lesions that radiate centrifugally from the optic nerve head.
