This 32YO male with known Marfan’s syndrome presented with one month of vision loss in his left eye. Examination revealed pathological myopia with bilateral spontaneously dislocated cataracts and a total rhegmatogenous retinal detachment (RRD) OS. Best-corrected vision was 20/80 OD and light perception OS.
Ultrawidefield photography shows a superior >270-degree giant retinal tear, total RRD, rolled edges, and a dislocated cataractous crystalline lens in the inferior vitreous. Emergent pars plana vitrectomy/lensectomy was planned, but unfortunately, he did not show for his surgery and was subsequently lost to follow-up.
