This 67YO male presented with asymptomatic retinal findings. There was no family history of ocular disease. Vision was 20/20 OU.
Color photography shows bilateral paravenous chorioretinal scarring with intraretinal pigment migration.
Learning Points:
Pigmented paravenous chorioretinal atrophy (PPCRA) is a rare condition characterized by paravenous pigment clumps with peripapillary and radial zones of RPE atrophy. It is bilateral, often asymmetric, with various causes, including genetic and pseudo-PPCRA (inflammatory, infectious, or unknown). Patients often have symptoms, usually nyctalopia, but most retain good vision, especially those without macular involvement. The underlying pathophysiology is likely a primary choroidopathy, which then causes overlying RPE and retinal changes. The chorioretinal changes are best visualized with fundus autofluorescence, which was unfortunately unavailable for our patient.
