Blog

BEST DISEASE WITH MACULAR NEOVASCULARIZATION

This healthy 11YO boy presented to us on 2/7/19 with asymptomatic retinal findings. Vision was 20/25 OD and 20/20 OS. Color photography of his right eye shows a partially scrambled vitelliform lesion consistent with Best vitelliform macular dystrophy (BVMD). A smaller, scarred, and atrophic lesion was noted in his left eye (not shown). He returned… Read More


DEGENERATIVE RETINOSCHISIS

This asymptomatic 40YO female was referred for a retinal detachment in her right eye. Vision was 20/20 OD and 20/20 OS in her normal OS. Pseudocolor SLO imaging shows a large area of inferotemporal degenerative retinoschisis (DRS) extending just into the distal macula. OCT scanning confirms schisis without retinal detachment. Observation was recommended. Learning Points:… Read More


MELANOCYTOMA

This 62YO female with type 2 diabetes was referred to us for diabetic retinopathy screening. Vision was 20/40 OD. Color photography shows moderate non-proliferative diabetic retinopathy with nasal lipid exudation. The inferior portion of the optic disc has a black discoloration deep to the vessels. OCT scanning through this lesion shows a dome-shaped hyperreflective mass… Read More


SEQUENTIAL GIANT RPE TEAR WITH SECONDARY EXUDATIVE RETINAL DETACHMENT

This 68YO male presented with sudden, painless decreased vision in his left eye 2 days ago. He gave a history of type 2 diabetes. Vision was 20/30 (6/9) in his normal OD and hand motion OS. Widefield photography shows a large curvilinear area of pigment loss (giant RPE tear) extending from the superotemporal into the… Read More


HARADA DISEASE

This 46YO male presented with 10 days of bilateral blurred vision with a left-sided headache. Vision was 20/200 OD and 20/20 OS. Anterior segments were normal. Pseudocolor SLO imaging shows bilateral swollen nerves and irregular macular chorioretinal folds. OCT scanning shows multifocal bacillary layer detachments, subretinal fluid, and an undulating, thickened choroid. Fluorescein angiography shows… Read More


X-LINKED RETINOSCHISIS

This 9YO boy presented with decreased vision in each eye since early childhood. Vision was 20/80 OU. Pseudocolor SLO imaging shows blunted foveal reflexes due to inner and outer nuclear layer schisis on OCT. Widefield imaging shows extension of the schisis cavities into the inferotemporal periphery, involving the inner retina with vitreous veils. These changes are… Read More


ISCHEMIC CRVO

This 78YO male presented with 1 week of sudden, painless decreased vision in his left eye. Vision was 20/20 in his normal OD and light perception OS. Despite iris neovascularization, intraocular pressure was normal. Color photography shows a hemorrhagic central retinal vein occlusion (CRVO) with variably confluent inner retinal hemorrhages and scattered nerve fiber layer… Read More


RETINOBLASTOMA

This previously healthy 2YO girl presented with leukocoria in her right eye. Family history was negative. Examination under anesthesia revealed a large smooth endophytic lesion filling more than half of the vitreous cavity, extending into the inferior macula. B-scan ultrasonography revealed intralesional calcifications. The left eye was normal. MRI showed no extra-ocular or CNS lesions…. Read More


PIGMENTED PARAVENOUS CHORIORETINAL ATROPHY

This healthy 55YO female presented with 2 years of mild bilateral vision loss. Family history was negative. Vision was 20/20 OD and 20/40 OS. Color photography shows bilateral paravenous chorioretinal scarring with intraretinal pigment migration. Learning Points: Pigmented paravenous chorioretinal atrophy (PPCRA) is a rare condition characterized by paravenous pigment clumps with peripapillary and radial… Read More


PNEUMATIC RETINOPEXY

This 56YO phakic male presented with floaters and a football-shaped nasal shadow in his right eye for one week. Vision was 20/20 bilaterally. Optos color RG imaging shows a superotemporal macula-on rhegmatogenous retinal detachment (RRD) from several tiny adjacent breaks within lattice. There were other areas of lattice degeneration superiorly, inferiorly, and inferotemporally within the… Read More